This image displays a newborn with a brown, flat area of pigment near the knee typical of café au lait macules. This image displays large, flat areas of color change typical of café au lait macules. This image displays a café au lait macule, a flat area of pigment that is usually not associated with other problems.  This café au lait mark appears as a light brown, flat area.
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Café au Lait Macule  A parent's guide for infants and babies

Picture of Café au Lait Macule: This image displays a newborn with a brown, flat area of pigment near the knee typical of café au lait macules. Divider line
This image displays a newborn with a brown, flat area of pigment near the knee typical of café au lait macules.
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Overview
A café au lait macule (CALM) is a well-defined, flat area that is darker in color than the rest of the skin (hyperpigmented). The term refers to the characteristic even (homogeneous) color of "coffee with milk," which may be light to dark brown.
  • Café au lait macules usually appear first in early childhood, although they may be present at birth. They may be single or multiple, and they increase in size as the person gets older.
  • Café au lait macules can be indicators of more extensive (multisystem) disease, particularly neurofibromatosis, a condition that is also marked by freckles in the armpit and groin regions, as well as neurofibromas.
Who's At Risk
Single café au lait macule lesions are present in 10–20% of the US population.
  • 1% of healthy young adults have up to 3 café au lait macules.
  • Lesions are more common in darker-skinned individuals (3% of Hispanic and 18% of black newborns have a café au lait macule), and these individuals have a darker "espresso" pigmentation, compared to those seen in whites.
Signs and Symptoms
Light-to-dark-brown, well-defined, even-colored, and often oval, flat lesions anywhere on the skin except for the linings (mucous membranes) of body cavities such as the mouth, nose, or genital areas.
Self-Care Guidelines
None necessary.
When to Seek Medical Care
While café au lait macules are common, see your child's doctor or a dermatologist if he or she has unidentified pigmented lesions.
Treatments Your Physician May Prescribe
No therapy is needed for café au lait macules. Lasers may be used for cosmetic concerns, although the color often comes back (recurs) after laser treatment.



References

Bolognia, Jean L., ed. Dermatology, pp.986-987, 1758-1759. New York: Mosby, 2003.

Freedberg, Irwin M., ed. Fitzpatrick's Dermatology in General Medicine. 6th ed. pp.772, 864-867, 2505. New York: McGraw-Hill, 2003.
Last Updated: 2 Sep 2009